Table 4.

List of inherited heart diseases and relevant International Statistical Classification of Diseases and Related Health Problems codes (ICD-9-AM)

Inherited heart condition	ICD diagnostic code and category
Arrhythmogenic right ventricular cardiomyopathy	I42.8 Other cardiomyopathies
Bicuspid aortic valve disease	Q23.83 Congenital bicuspid aortic valve
Brugada syndrome	I49.8 Other specified cardiac arrhythmias
Catecholaminergic polymorphic ventricular tachycardia	I47.2 Ventricular tachycardia
Familial dilated cardiomyopathy	I42.0 Dilated cardiomyopathy
Familial hypercholesterolaemia	E78.0 Pure hypercholesterolaemia
Familial restrictive cardiomyopathy	I42.5 Other restrictive cardiomyopathy
Hypertrophic cardiomyopathy	I42.1 Obstructive hypertrophic cardiomyopathy I42.2 Other hypertrophic cardiomyopathy Q24.89 Other specified congenital malformations of the heart
Left ventricular non-compaction	I42.8 Other cardiomyopathies I42.9 Cardiomyopathy, unspecified
Long QT syndrome	R94.3 Abnormal results of cardiovascular function studies
Marfan syndrome	Q87.4 Marfan syndrome