TABLE I.
Demographics
| Demographics | n=50 |
|---|---|
| Male | 20 (40) |
| Age at testing (years)† | 12.1 (4.1–64.1) |
| FEV1 % predictedǂ | 91.7 (25.6) |
| FEV1 z-scoreǂ | −0.66 (2.1) |
| †Median (range), ǂMean (SD) | |
| Presenting symptoms (most common findings) | |
| Cough | 38 (76) |
| Daily cough | 22 (58) |
| Nasal congestion | 25 (50) |
| Pneumonia/bronchitis | 23 (46) |
| Sinusitis | 23 (46) |
| Rhinorrhea | 17 (34) |
| Unresponsive asthma | 17 (34) |
| Neonatal respiratory distress | 9 (18) |
| Situs inversus totalis | 5 (10) |
| Nasal ciliary biopsy | |
| Normal ultrastructure | 11 (22) |
| Outer dynein arm defect | 2 (4) |
| Central pair defect | 2 (4) |
| PCD determination | |
| Confirmed PCD | 4 (8) |
| Probable PCD | 6 (12) |
| Other diagnosis/undefined | 40 (80) |
Values are mean (SD) or median (range) for continuous variables and frequency (%) for categorical variables