Table 5. Frequency of hepatic and biliary tract manifestations in patients with cystic fibrosis.

Organ	Approximate proportion, %
Liver Increased liver enzymes Hepatic steatosis Focal biliary cirrhosis Multilobular biliary cirrhosis Neonatal cholestasis Bile duct stenosis Sclerosing cholangitis Cholangiocarcinoma	10-35 20-60 11-70 5-15 < 2 < 2 < 1 rare
Gallbladder Cholelithiasis and cholecystitis Microvesicules	10-30 24-50

Adapted from Debray et al.⁽¹⁸⁹⁾