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. Author manuscript; available in PMC: 2017 Dec 4.
Published in final edited form as: Ann Neurol. 2016 Feb 12;79(3):379–386. doi: 10.1002/ana.24572

Table 1. Clinical features in cases of SDH-related leukoencephalopathy.

Clinical Features Percentage of Cases
Age of Onset Average: 11.21 mo.
Range: Birth – 20 mo.
Consanguinity 67% (13/19)
Abrupt Decompensation 72% (14/19)
Microcephaly 50% (8/17)
Truncal Hypotonia 75% (13/17)
Limb spasticity 89% (17/19)
Ataxia 92% (12/14)
Dystonia 25% (4/17)
Acquired Independent Ambulation 25% (5/17)
Current Functional Level 7 Individuals with a severe spastic tetraparesis
11 Individuals with moderate or severe cognitive impairment
5 Individuals died at mean age of 5 years

Key: mo. = month, N/A=Not Available, yrs.= years