Table 4.
Description of the 17 patients who received a physician diagnosis of pSS but fulfilled neither classification criteria set
| Pt. | Age | Durationa | Eyeb | Mouthc | ESSDAI | ESSDAI domainsd | Other AID | Low UWSF | Schirmer | VB ≥ 4 | SGB | ANA | SSA/SSB | RF | IgG | SGUS |
|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
| 1 | 52 | 4 | 1 | 1 | 0 | / | 0 | 0 | 0 | / | 1 | 640 | 0 | 0 | 11.6 | 1 |
| 2 | 25 | 0 | 0 | 0 | 6 | H | 0 | 0 | 0 | 0 | 0 | 160 | 1 | 1 | 11.6 | 0 |
| 3 | 63 | 1 | 1 | 1 | 0 | / | 0 | / | 0 | 0 | 1 | 1 280 | 0 | 0 | 6,9 | 1 |
| 4 | 69 | 3 | 1 | 1 | 10 | PNS, R | 0 | 0 | 0 | / | 1 | 0 | 0 | 0 | 9,8 | 0 |
| 5 | 48 | 6 | 1 | 1 | 19 | A, CNS, B | Thyroiditis | 0 | 0 | / | 0 | 0 | 0 | 0 | 22.0 | 0 |
| 6 | 39 | 3 | 1 | 0 | 2 | A | 0 | 0 | 0 | / | 1 | 1 280 | 0 | 0 | 11.9 | 1 |
| 7 | 47 | 24 | 1 | 1 | 4 | H, B | 0 | / | 1 | / | 0 | 0 | 0 | 1 | 31.4 | 0 |
| 8 | 60 | 20 | 1 | 1 | 8 | A, PNS, B | 0 | 0 | 0 | / | 0 | 1 280 | 1 | 0 | 18.9 | 1 |
| 9 | 50 | 13 | 1 | 1 | 14 | A, PNS, G | 0 | 0 | 0 | 0 | 1 | 160 | 0 | 0 | 11.4 | 0 |
| 10 | 50 | 1 | 1 | 1 | 4 | H | 0 | 0 | 0 | / | 0 | 1 280 | 0 | 0 | 10.7 | 0 |
| 11 | 55 | 7 | 1 | 1 | 0 | / | 0 | 0 | 0 | 0 | 1 | 160 | 0 | 0 | 8.8 | 0 |
| 12 | 61 | 5 | 1 | 1 | 0 | / | 0 | 0 | 0 | 0 | 1 | 0 | 0 | 0 | 11.2 | 0 |
| 13 | 49 | 2 | 1 | 1 | 0 | / | 0 | 0 | 0 | 0 | 1 | 160 | 0 | 0 | 10.1 | 1 |
| 14 | 51 | 4 | 1 | 0 | 2 | G | 0 | 0 | 0 | 0 | 0 | 0 | 1 | 1 | 6.7 | 1 |
| 15 | 63 | 1 | 1 | 1 | 8 | A, C | 0 | 0 | 0 | 0 | 1 | 160 | 0 | 0 | 11.0 | 0 |
| 16 | 65 | 28 | 1 | 1 | 1 | B | 0 | 0 | 0 | 1 | 0 | 320 | 0 | 0 | 7.7 | 0 |
| 17 | 51 | 1 | 1 | 1 | 12 | R, B | 0 | 0 | 0 | 0 | 0 | 320 | 1 | 0 | 15.9 | 1 |
pSS primary Sjögren’s syndrome Pt patient, ESSDAI EULAR pSS Disease Activity Index, AID autoimmune disease, UWSF unstimulated whole salivary flow, VB van Bijsterveld score, SGB salivary gland biopsy, ANA anti-nuclear antibodies, RF rheumatoid factors, SGUS salivary gland ultrasonography, SSA Anti-Sjögren's-syndrome-related antigen A
aSymptom duration in years
bSubjective ocular dryness
cSubjective oral dryness
d A articular, P pulmonary, PNS peripheral nervous system, R renal, G glandular, C cutaneous, L lymphadenopathy, H hematological, B biological