Table 5.
Sub-diagnosis | Frequency | Reclassified as |
---|---|---|
Idiopathic | 63 | Kept the same |
Heritable – BMPR2 | 3 | Other |
Heritable – ALK1 endoglin | 2 | Other |
Heritable – unknown | 3 | Other |
Drugs and toxins induced | 1 | Other |
Connective tissue disease | 37 | Kept the same |
HIV infection | 3 | Other |
Portal hypertension | 6 | Other |
Congenital heart disease | 48 | Kept the same |
Chronic hemolytic anemia | 1 | Other |
Pulmonary veno-occlusive disease | 5 | Other |
Chronic thromboembolic – proximal | 61 | Kept the same |
Chronic thromboembolic – distal | 35 | Kept the same |
Sarcoidosis | 8 | Other |
Pulmonary Langerhans cell histiocytosis | 1 | Other |
Vasculitis | 1 | Other |
Fibrosing mediastinitis | 1 | Other |
Chronic renal failure on dialysis | 2 | Other |
Other | 1 | Other |