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. Author manuscript; available in PMC: 2018 Dec 1.
Published in final edited form as: Ann Rheum Dis. 2017 Oct 27;76(12):1955–1964. doi: 10.1136/annrheumdis-2017-211468

Table 3.

Comparison of physician-diagnosed idiopathic inflammatory myopathies (IIM) subgroups with IIM subgroups defined according to the classification tree among patients meeting the EULAR/ACR classification criteria for IIM

Physician-diagnosed subgroups Classification tree subgroups* Total
JDM DM ADM IBM PM
JDM 235 0 0 0 0 235
DM 0 191 6 2 15 214
ADM 1 1 30 0 0 32
IBM 0 0 0 66 5 71
PM 0 7 0 3 131 141
IMNM 0 0 0 0 10 10

Total 236 199 36 71 161 703

% of all IIM 33.6 28.3 5.1 10.1 22.9

% of adult IIM 42.6 7.7 15.2 34.5
*

Classification of IIM by the EULAR/ACR classification criteria for IIM, using a 55% probability cutoff for classification, followed by the classification tree for sub-classification.

JDM, juvenile dermatomyositis; DM, dermatomyositis; ADM, amyopathic dermatomyositis; IBM, inclusion body myositis; PM, polymyositis; IMNM, immune-mediated necrotizing myopathy.