Table 1.

Criteria for clinical diagnosis of Cogan’s syndrome

Mandatory criteria	Prevalent additional criteria	Possible additional criteria
Sensorineural hearing loss	Vertigo, dizziness, ataxia	Vasculitis
Inflammatory ocular disease	Tinnitus	Positivity for systemic inflammatory markers
Alternative causes of inflammation or infection ruled out	Nonspecific systemic symptoms such as weight loss, fever, lymphadenopathy, and headache

Note: Mandatory and on prevalent and possible additional criteria for clinical diagnosis of Cogan’s syndrome.