Table 1.

Mitochondrial Oxygen Consumption Rates (OCR) in intact MCAD-deficient patient fibroblasts.

	Mitochondrial Oxygen Consumption Rates pmol/min/20,000 cells (% of Control Values)
	OCR-Basal	OCR-O	OCR-F	OCR-R	FCCP-stimulated
Control	51 ± 12	19 ± 5	89 ± 24	15 ± 6	74 ± 19
Patient 1 (P1)	28 ± 5* (55%)	11 ± 2* (57%)	42 ± 9* (47%)	9 ± 3* (63%)	32 ± 8* (44%)
Patient 2 (P2)	40 ± 8* (78%)	14 ± 3* (73%)	53 ± 11* (60%)	12 ± 2 (79%)	42 ± 9* (56%)

OCR-O = OCR with oligomycin; OCR-F = OCR with FCCP; OCR-R = OCR with rotenone.

FCCP-stimulated = OCR-F minus OCR-R.

Each condition was performed in at least 14 wells on the same plate.

*p < 0.01.