Table 1. Clinical, biological and follow-up data of the 22 patients with DFSP or DFSP-T.
| Patient | Diagnosis | Age at diagnosis (years) | Sex | Tumor site | Largest Tumor size (cm) | Treatment | Follow-up duration (months) | Metastatic disease | Status at last follow-up |
|---|---|---|---|---|---|---|---|---|---|
| 1 | DFSP | 54 | M | Shoulder | 2.5 | Surgery | 38 | No | aned |
| 2 | DFSP | 37 | F | Thigh | 2.5 | Surgery | 36 | No | aned |
| 3 | DFSP | 33 | M | Thigh | 2 | Surgery | 39 | No | aned |
| 4 | DFSP | 27 | F | Chest | 2 | Surgery | 38 | No | aned |
| 5 | DFSP | 50 | F | Thigh | 2 | Surgery | 40 | No | aned |
| 6 | DFSP | 40 | M | Face | 3 | Surgery | 26 | No | aned |
| 7 | DFSP | 55 | F | Shoulder | 1.5 | Surgery | 39 | No | aned |
| 8 | DFSP | 44 | M | Chest | 7 | Surgery | 10 | No | aned |
| 9 | DFSP | 41 | F | Back | 1.5 | Surgery | 42 | No | aned |
| 10 | DFSP | 47 | M | Chest | 3 | Surgery | 24 | No | aned |
| 11 | DFSP | 51 | F | Arm | 6.5 | Surgery | 39 | No | aned |
| 12 | DFSP | 29 | M | Back | 9 | Surgery | 156 | No | aned |
| 13 | DFSP-T (FS) | 21 | M | Shoulder | 2 | Surgery | 38 | No | aned |
| 14 | DFSP-T (FS) | 33 | F | Thigh | 4 | Surgery | 25 | No | aned |
| 15 | DFSP-T (FS) | 54 | F | Abdomen | 20 | Imatinib, surgery and radiotherapy | 110 | No | aned |
| 16 | DFSP-T (FS) | 48 | M | Thigh | 4.5 | Surgery | 24 | No | aned |
| 17 | DFSP-T (FS) | 23 | F | Face | 15 | Imatinib | 120 | Yes | awd |
| 18 | DFSP-T (FS) | 68 | M | Abdomen | 8 | Surgery and radiotherapy | 51 | No | aned |
| 19 | DFSP-T (FS) | 49 | F | Back | 6 | Surgery | 40 | No | aned |
| 20 | DFSP-T (FS) | 36 | M | Thigh | 9 | Surgery | 66 | No | aned |
| 21 | DFSP-T (UPS) | 83 | F | Leg | 17 | Surgery | 40 | No | aned |
| 22 | DFSP-T (UPS) | 65 | F | Chest | 16 | Surgery | 3 | Yes | dod |
Abbreviations: DFSP, dermatofibrosarcoma protuberans; DFSP-T, transformed dermatofibrosarcoma protuberans; FS, fibrosarcoma; UPS, undifferentiated pleomorphic sarcoma; M, male; F, female; aned, alive with no evidence of disease; awd, alive with disease; dod, dead of disease.