Table 2.
WHO sub-categorizations (& actual clinical diagnoses), n(%) |
Group 1 patients (n=64) |
---|---|
Group 1.1 (idiopathic) | 28(43.8%) |
Group 1.2 (BMPR2) | 2(3.1%) |
Group 1.3 (Anorexigen-induced) | 1(1.6%) |
Group 1.4.1 (SLE, Scleroderma [including CREST], polymyositis/dermatomyositis, poly mystic with overlap syndrome, ill defined [RA vs Sjögren’s]) | 23(36%) |
Group 1.4.3 (portal hypertension) | 5(7.8%) |
Group 1.4.4 (ASD) | 5(7.8%) |