Table 4.
Clinical characteristics of ataxic non-psychotic autopsy study cohort (n = 22)
| SCA type | No. for ataxia type |
|---|---|
| Familial ataxia, gene unknown | 8 |
| Episodic ataxia type II (genetically confirmed) | 1 |
| Friedrich’s ataxia (genetically confirmed) | 2 |
| SCA 2 (genetically confirmed) | 2 |
| SCA 3 (genetically confirmed) | 5 |
| SCA 5 (genetically confirmed) | 1 |
| Fragile X tremor ataxia syndrome (genetically confirmed) with Alzheimer’s pathology | 1 |
| SCA 17 (genetically confirmed) | 1 |
| Ataxia telangiectasia (genetically confirmed) | 1 |