Fig 2. Chest computed tomography scans in Hermansky-Pudlak syndrome pulmonary fibrosis patients before and after lung transplantation.

Representative computed tomography scan images of the chest from one patient with Hermansky-Pudlak syndrome pulmonary fibrosis showing diffuse bilateral interstitial infiltrates at the time of referral for lung transplantation (A) and 6 years after bilateral lung transplant surgery (B). Representative computed tomography scan images of the chest from another patient with Hermansky-Pudlak syndrome pulmonary fibrosis showing bilateral pulmonary fibrosis before lung transplantation (C) and 1.5 years after bilateral lung transplant surgery (D). Post-operative surgical changes are found, but there is no radiographic evidence of recurrence of Hermansky-Pudlak syndrome pulmonary fibrosis in the lung allografts.