TABLE. Number and percentage of identified cases of amyotrophic lateral sclerosis (N = 15,927) and estimated prevalence, by age group, sex, race, and geographic region — National ALS Registry, United States, 2014.
Characteristic | Population* | No. (%) ALS cases | Prevalence estimate (cases per 100,000 population), % (95% CI) |
---|---|---|---|
Age group (yrs) | |||
18–39 | 94,902,312 | 506 (3.2) | 0.5 (0.5–0.6) |
40–49 | 41,479,525 | 1,587 (10.0) | 3.8 (3.5–4.2) |
50–59 | 44,082,258 | 3,492 (21.9) | 7.9 (7.4–8.4) |
60–69 | 33,891,398 | 4,861 (30.5) | 14.3 (13.7–15.0) |
70–79 | 18,995,348 | 3,807 (23.9) | 20.0 (19.2–20.9) |
≥80 | 11,922,597 | 1,623 (10.2) | 13.6 (13.1–14.2) |
Unknown | — | 51 (0.3) | — |
Sex | |||
Males | 156,936,487 | 9,821 (18.6) | 6.3 (6.1–6.4) |
Females | 161,920,569 | 5,854 (36.8) | 3.6 (3.5–3.7) |
Unknown | — | 252 (1.6) | — |
Race | |||
White | 233,963,128 | 12,660 (79.5) | 5.4 (5.2–5.5) |
Black | 40,379,066 | 988 (6.2) | 2.4 (2.3–2.6) |
Other | — | 863 (5.4) | — |
Unknown | — | 1,416 (8.9) | — |
U.S. Census region† | |||
Midwest | 67,745,108 | 3,832 (24.1) | 5.7 (5.4–5.9) |
Northeast | 56,152,333 | 3,075 (19.3) | 5.5 (5.2–5.8) |
South | 119,771,934 | 5,682 (35.7) | 4.7 (4.6–4.9) |
West | 75,187,681 | 3,252 (20.4) | 4.3 (4.1–4.5) |
Unknown | — | 86 (0.5) | — |
Total | 318,857,056 | 15,927 | 5.0 (4.9–5.1) |
Abbreviations: ALS = amyotrophic lateral sclerosis; CI = confidence interval.
* From 2014 U.S. Census data.
† Northeast: Connecticut, Maine, Massachusetts, New Hampshire, New Jersey, New York, Pennsylvania, Rhode Island, Vermont; South: Alabama, Arkansas, Delaware, District of Columbia, Florida, Georgia, Kentucky, Louisiana, Maryland, Mississippi, North Carolina, Oklahoma, South Carolina, Tennessee, Texas, Virginia, West Virginia; Midwest: Iowa, Illinois, Indiana, Kansas, Michigan, Minnesota, Missouri, Nebraska, North Dakota, Ohio, South Dakota, Wisconsin; West: Alaska, Arizona, California, Colorado, Hawaii, Idaho, Montana, Nevada, New Mexico, Oregon, Utah, Washington, Wyoming.