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. 2018 Feb 23;67(7):216–218. doi: 10.15585/mmwr.mm6707a3

TABLE. Number and percentage of identified cases of amyotrophic lateral sclerosis (N = 15,927) and estimated prevalence, by age group, sex, race, and geographic region — National ALS Registry, United States, 2014.

Characteristic Population* No. (%) ALS cases Prevalence estimate (cases per 100,000 population), % (95% CI)
Age group (yrs)
18–39 94,902,312 506 (3.2) 0.5 (0.5–0.6)
40–49 41,479,525 1,587 (10.0) 3.8 (3.5–4.2)
50–59 44,082,258 3,492 (21.9) 7.9 (7.4–8.4)
60–69 33,891,398 4,861 (30.5) 14.3 (13.7–15.0)
70–79 18,995,348 3,807 (23.9) 20.0 (19.2–20.9)
≥80 11,922,597 1,623 (10.2) 13.6 (13.1–14.2)
Unknown 51 (0.3)
Sex
Males 156,936,487 9,821 (18.6) 6.3 (6.1–6.4)
Females 161,920,569 5,854 (36.8) 3.6 (3.5–3.7)
Unknown 252 (1.6)
Race
White 233,963,128 12,660 (79.5) 5.4 (5.2–5.5)
Black 40,379,066 988 (6.2) 2.4 (2.3–2.6)
Other 863 (5.4)
Unknown 1,416 (8.9)
U.S. Census region
Midwest 67,745,108 3,832 (24.1) 5.7 (5.4–5.9)
Northeast 56,152,333 3,075 (19.3) 5.5 (5.2–5.8)
South 119,771,934 5,682 (35.7) 4.7 (4.6–4.9)
West 75,187,681 3,252 (20.4) 4.3 (4.1–4.5)
Unknown 86 (0.5)
Total 318,857,056 15,927 5.0 (4.9–5.1)

Abbreviations: ALS = amyotrophic lateral sclerosis; CI = confidence interval.

* From 2014 U.S. Census data.

Northeast: Connecticut, Maine, Massachusetts, New Hampshire, New Jersey, New York, Pennsylvania, Rhode Island, Vermont; South: Alabama, Arkansas, Delaware, District of Columbia, Florida, Georgia, Kentucky, Louisiana, Maryland, Mississippi, North Carolina, Oklahoma, South Carolina, Tennessee, Texas, Virginia, West Virginia; Midwest: Iowa, Illinois, Indiana, Kansas, Michigan, Minnesota, Missouri, Nebraska, North Dakota, Ohio, South Dakota, Wisconsin; West: Alaska, Arizona, California, Colorado, Hawaii, Idaho, Montana, Nevada, New Mexico, Oregon, Utah, Washington, Wyoming.