Table 1.
Enzymatic activity measured in lymphocytes and fibroblasts
Cell type | LCHAD activity (nmol/(mg min protein)) | Reference value | LCKAT activity (nmol/(mg min protein)) | Reference value |
---|---|---|---|---|
Fibroblasts | 12 | 34–114 | 6 | 58–110 |
Lymphocytes | 6 | 22–74 | 2 | 23–43 |
LCHAD long-chain 3-hydroxyacyl-CoA dehydrogenase, LCKAT long-chain 3-ketoacyl-CoA thiolase