Table 1.

Baseline characteristics

Number	107
Age	45.0 ± 16.6
Male	53 (49.5%)
Time of TTCE
Screening for HHTa	57 (53.3%)
Follow-up of pulmonary RLSb	50 (46.7%)
Definite HHTc	77 (72.0%)
HHT type
– Type 1	32 (29.9%)
– Type 2	36 (33.6%)
– SMAD4	6 (5.6%)
– Unknown	3 (2.8%)

Data are presented as number (%) or mean ± standard deviation

HHT hereditary haemorrhagic telangiectasia, RLS right-to-left shunt, SMAD4 SMAD family member 4, TTCE transthoracic contrast echocardiography

^aTTCE made to screen for pulmonary RLS

^bTTCE made at regular 5 year follow-up

^cBased on genetic testing or clinical criteria [1]