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. 2018 Mar 25;11(1):52–56. doi: 10.3400/avd.ra.18-00002

Table 1 Criteria for BD.

A: Japan (Minister of Health, Labour and Welfare)1)
Major symptoms
1. Recurrent oral aphthoid ulcer
2. Skin lesions
3. Ocular symptoms
4. Genital ulcer
Minor symptoms
1. Arthritis without deformity and ankylosis
2. Epididymitis
3. Gastrointestinal lesions such as ileocecal ulcers
4. Vascular lesions
5. Central nervous system lesion
Complete type: 4 major symptoms during the course
Incomplete type: 3 major symptoms, 2 major+2 minor symptoms, or typical ocular symptoms+1 major symptom or 2 minor symptoms
B: International Study Group12)
Major criteria
Recurrent oral ulceration
Minor criteria
1. Recurrent genital ulceration
2. Eye lesions
3. Skin lesions
4. Pathergy test
Major+2 minor criteria indicate BD
C: International Criteria for BD13)
Ocular lesions 2 points
Oral aphthosis 2 points
Genital aphthosis 2 points
Skin lesions 1 point
Central nervous system involvement 1 point
Vascular manifestations 1 point
Positive pathergy test 1 point

Scoring ≥4 indicates BD. BD: Behçet’s disease