Table 1.
Patient | Gene | DNA (NG_005895.1) | Protein (NP_000539.2) | Exon | Age of Epilepsy Onset | Autism | Intellec Disability | Age at dermal biopsy | Biopsy skin lesion |
---|---|---|---|---|---|---|---|---|---|
TSP20 | TSC2 | g.11900T>A | p.Cys203Ter | 6/41 | 6 months | Y | Y | 6 years | Hypopigmented macule |
TSP23 | TSC2 | g.34854C>T | p.Arg1032Ter | 26/41 | 6 months | Y | Y | 2 years | Hypopigmented macule |
TSP31 | TSC2 | g.40172C>T | p.Gln1419Ter | 33/41 | 2 months | Y | Y | 12 years | Shagreen patch |