Table 1. Patients baseline characteristics.
| Number of subjects | 16 |
|---|---|
| Age (years) | 11.1±2.4 |
| Male/female | 9/7 |
| Weight (kg) | 39.2±10.3 |
| Height (cm) | 144±14.2 |
| BMI (kg/m2) | 18.5±2.2 |
| FEV1 (l/s) | 2.27±0.61 |
| FEV1 (%) | 106±11.9 |
| TLC (l) | 3.65±0.92 |
| TLC (%) | 108±11.2 |
| RV (l) | 0.88±0.35 |
| RV (%) | 131±38.4 |
| RV/TLC (%) | 24±5.3 |
| PA positive | 2 |
| MRSA positive | 3 |
| Pancreatic insufficiency | 16 |
| Homozygous F508del | 12 |
BMI = body mass index, FEV1 = forced expiratory volume in 1s, TLC = total lung capacity, RV = residual volume, RV/TLC = percentage of residual volume/total lung capacity. Percentage values refer to the predicted volumes. PA = chronic Pseudomonas aeruginosa infection; MRSA = chronic methicillin resistant Staphylococcus aureus infection.