Table 1.

Characteristics of life-threatening AOSD

	n (%)
Characteristics of patients
Age, years (median)	36 (18–64)
Male	12 (60%)
First episode	18 (90%)
AOSD features
Fever	20 (100%)
Rash	13 (65%)
Sore throat	13 (65%)
Arthromyalgia	17 (85%)
Arthritis	3 (15%)
Hepatosplenomegaly	13 (65%)
Organ manifestations
Respiratory
Acute respiratory failure	15 (75%)
Lung infiltrate	12 (60%)
Pleural effusion	12 (60%)
Cardiocirculatory
Shock	10 (50%)
Myocarditis	8 (40)
Pericarditis	10 (50%)
Tamponade	3 (16%)
Hematologic
Disseminated intravascular coagulation	10 (50%)
Hemophagocytosis	8 (40%)
Thrombotic microangiopathy	1 (5%)
Other
Acute kidney injury	7 (35%)
Neurologic dysfunction	5 (25%)
Severe hepatitis	3 (15%)
Multiple organ failure	8 (40%)
Death	2 (10%)