TABLE 4.

Survival data

	All patients#			No or moderate BD¶			Severe BD+
	NIV	No NIV	p-value	NIV	No NIV	p-value	NIV	No NIV	p-value
Patients	120	20		105	14		15	6
Survival from ALS onset months	43.00 (38.13–47.86)	28.00 (21.40–34.57)	0.001	43.00 (39.01–46.98)	33.00 (26.64–39.35)	0.002	40.00 (29.64–50.35)	16.00 (5.19–26.80)	0.002
Survival from NIV months	18.50 (12.62–24.38)	3.00 (0.82–5.18)	0.001	20.00 (13.71–26.28)	3.00 (0.55–5.44)	0.0001	13.00 (9.49–16.50)	3.00 (0.85–5.14)	0.001

Data are presented as mean (95% CI) unless otherwise stated. NIV: noninvasive ventilation; BD: bulbar dysfunction; ALS: amyotrophic lateral sclerosis. ^#: n=140; ^¶: n=119; ⁺: n=21.