Table 1.
Diagnosis | Criteria |
---|---|
Definitive | Diffuse or local swelling or multiple organs |
Serum IgG4 levels ≥ 135 mg/dL | |
Histology: | |
(1) Lymphoplasmacytic infiltrate and fibrosis (2) IgG4+ plasma cells: ratio of IgG4+/IgG+ cells > 40%, and >10 IgG4+ plasma cells/high-power field | |
| |
Probable | Diffuse or local swelling or multiple organs |
Histology: | |
(1) Lymphoplasmacytic infiltrate and fibrosis (2) IgG4+ plasma cells: ratio of IgG4+/IgG+ cells > 40%, and >10 IgG4+ plasma cells/high-power field | |
| |
Possible | Diffuse or local swelling or multiple organs |
Serum IgG4 levels ≥ 135 mg/dL |