Skip to main content
. 2018 Apr 1;2018:6936727. doi: 10.1155/2018/6936727

Table 1.

Diagnostic criteria for IgG4-related disease (modified after Umehara et al. [4]).

Diagnosis Criteria
Definitive Diffuse or local swelling or multiple organs
Serum IgG4 levels ≥ 135 mg/dL
Histology:
(1) Lymphoplasmacytic infiltrate and fibrosis
(2) IgG4+ plasma cells: ratio of IgG4+/IgG+ cells > 40%, and >10 IgG4+ plasma cells/high-power field

Probable Diffuse or local swelling or multiple organs
Histology:
(1) Lymphoplasmacytic infiltrate and fibrosis
(2) IgG4+ plasma cells: ratio of IgG4+/IgG+ cells > 40%, and >10 IgG4+ plasma cells/high-power field

Possible Diffuse or local swelling or multiple organs
Serum IgG4 levels ≥ 135 mg/dL