Table 1.
Current Classification of Vascular Anomalies*
| TUMORS | MALFORMATIONS | |||
|---|---|---|---|---|
|
| ||||
| Simple | Combined | Major Named Vessels | Associated With Other Anomalies | |
|
| ||||
| Benign | Capillary | Capillary-venous | Aneurysm | CLOVES |
| Infantile hemangioma | Cutis marmorata telangiectatica congenita | Capillary-lymphatic | Atresia | Klippel-Trenaunay |
| Congenital hemangioma | Capillary-arteriovenous | Ectasia | Megalencephaly-capillary malformation | |
| Pyogenic granuloma | Fading stain | Lymphatic-venous | Stenosis | Mafucci |
| Infantile myofibroma | Capillary-lymphatic-venous | Parkes Weber | ||
| Enzinger hemangioma | Lymphatic | Capillary-lymphatic-arteriovenous | Proteus | |
| Macrocystic | Capillary-venous-arteriovenous | PTEN hamartoma | ||
| Intermediate | Microcystic | Capillary-lymphatic-venous-arteriovenous | Sturge-Weber | |
| Kaposiform hemangioendothelioma | Generalized | |||
| Tufted angioma | Gorham-Stout | |||
| Primary lymphedema | ||||
| Malignant | ||||
| Angiosarcoma | Venous | |||
| Epitheliod hemangioendothelioma | Cutaneoumucosal | |||
| Glomuvenous | ||||
| Cerebral cavernous | ||||
| Blue rubber bleb nevus | ||||
| Fibro adipose | ||||
| Verrucous | ||||
| Arteriovenous | ||||
| Capillary malformation-arteriovenous malformation | ||||
| Hereditary hemorrhagic telangiectasia | ||||
*
Adapted from “Vascular Anomalies Classification: Recommendations From the International Society for the Study of Vascular Anomalies,” Wassef et al., 2015, Pediatrics, 136, p. 203–214.