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. 2018 Mar 13;5(1):293–301. doi: 10.1007/s40744-018-0103-9

Table 3.

Diseases other than rheumatoid arthritis associated with positive rheumatoid factor or anti-CCP antibody

Positive rheumatoid factor
Autoimmune disease
 Rheumatoid arthritis
 Primary Sjögren’s syndrome
 Mixed cryoglobulinemia (hepatitis C)
 Systemic lupus erythematosus
 Mixed connective tissue disease
 Polymyositis/dermatomyositis
 Systemic sclerosis
Infection
 Subacute bacterial endocarditis
 Hepatitis (A, B, and C)
 Epstein–Barr virus and  cytomegalovirus infections
 Tuberculosis
 Syphilis
Miscellaneous
 Sarcoidosis 28
 Waldenström’s macroglobulinemia 25
 Liver cirrhosis 25
 Interstitial lung diseases
Positive anti-CCP antibody
 Systemic lupus erythematosusa
 Sjögren’s syndromea
 Psoriatic arthritis
 Tuberculosis
 Hepatitis C
 Chronic obstructive pulmonary disease
 Alpha 1 anti-trypsin deficiency

aMore likely in erosive disease (possible RA overlap syndrome)