Table 1.

Neuromuscular Scoring Criteria

Posture	Ataxia	Seizure Activity	Tone
0: normal	0: normal	0: normal	0: normal
1: low posture	1: ataxia, no falling	1: twitches/shuddering	1: mild hypotonia
2: lying on ground, straight posture	2: ataxia with falling	2: active myoclonic seizure	2: moderate hypotonia
3: lying on ground, leaning posture			3: severe hypotonia