Table 5.
LTX: Demographics and Outcomes
| Feature | FIC1 | BSEP | P |
|---|---|---|---|
| # Undergoing LTX | 24 | 33 | |
| Median years with LTX (IQR) | 3.6 (1.1‐7.1) n = 24 | 3.6 (1.1‐6.1) n = 33 | 0.99 |
| Median age (years) at LTX (IQR) | 5.8 (3.0‐12.1) n = 24 | 3.1 (1.9‐5.8) n = 33 | 0.010 |
| Median year of birth (full range) | 1991 (1976‐1999) n = 24 | 1996 (1978‐2003) n = 33 | 0.030 |
| Proportion male | 8/24 (33%) | 16/33 (48%) | 0.29 |
| # With older affected sibling | 4/24 (17%) | 5/33 (15%) | 1.00 |
| # Died post‐LTX | 3/24 (13%) | 0/33 (0%) | 0.07 |
| # Requiring retransplant | 1/24 (4%) | 4/33 (12%) | 0.39 |
| # With rejection | 15/21 (71%) | 22/31 (71%) | 1.0 |
| # With hepatic steatosis | 19/21 (90%) | 2/31 (6%) | <0.0001 |
| # With diarrhea | 17/21 (81%) | 2/29 (7%) | <0.0001 |
| # Requiring parenteral nutrition | 3/20 (15%) | 0/29 (0%) | 0.062 |
| # With pancreatitis or pancreatic insufficiency |
8/20 (40%) 7 pancreatitis 1 insufficiency |
0/29 (0%) | 0.0003 |
P values <0.05 are noted in bold.