Table 1. Clinical characteristics.
Items | Clinical characteristics |
---|---|
Age (years), mean ± SD | 58±13 |
Sex (n) | Male (n=16), female (n=44) |
Disease duration (months), median (range) | 81 (10–564) |
Disease subsets (n) | lSSc (n=33), dSSc (n=27) |
Extent of skin fibrosis assessed by the modified Rodnan Skin score, median (range)/51 | 9.5 (0–31)/51 |
Antibody profile (n) | ANA positive (n=59) ACA positive (n=16) Scl-70 positive (n=23) RNA-polymerase III positive (n=7) |
Major organ involvement except lung fibrosis ± (n) | Heart (n=18) Gastrointestinal tract (n=10) Pulmonary arterial hypertension (n=5) |
Lung function parameters, mean ± SD (range) | |
FVC (%) predicted | 92.49±22.1 (41–136) |
FEV1 (%) predicted | 89.76±19.74 (42–122.2) |
TLC (%) predicted | 90.74±2.83 (31.1–139) |
DCLO (%) predicted | 76.32±19.3 (40–123) |