Table 3. Clinical characteristics of atypical and plexiform neurofibromas.
| Characteristic | ATRX positive (N = 28) | ATRX mosaic (N = 2) | Total (N = 30) |
|---|---|---|---|
| Sex—no. (%) | |||
| Male | 10 (36) | 1 (50) | 11 (37) |
| Female | 18 (64) | 1 (50) | 19 (63) |
| Age at diagnosis—yr | |||
| Median | 21 | 11 | 23 |
| Range | 7–67 | 4–27 | 4–67 |
| Age Category—no. (%) | |||
| <18 yo | 9 (32) | 1 (50) | 10 (33) |
| 18 to 65 yo | 18 (64) | 1 (50) | 19 (63) |
| >65 yo | 1 (4) | 0 | 1 (4) |
| NF Status—no. (%) | |||
| NF1 | 26 (93) | 2 (100) | 28 (94) |
| Sporadic | 1 (3) | 0 | 1 (3) |
| Not Reported | 1 (3) | 0 | 1 (3) |
| Tumor Type—no.(%) | |||
| Atypical Neurofibroma | 9 (32) | 0 | 9 (30) |
| Plexiform Neurofibroma | 19 (68) | 2 (100) | 21 (70) |
There were no ATRX negative patients in the above tumor types.