Table 2.
Names of Previously-Recognized Conditions That Comprise Or May Comprise Parts of the IgG4-Related Disease Spectrum.
| Mikulicz’s disease | |
| Küttner’s tumor | |
| Riedel’s thyroiditis | |
| Eosinophilic angiocentric fibrosis | |
| Multifocal fibrosclerosis | |
| Lymphoplasmacytic sclerosing pancreatitis / autoimmune pancreatitis | |
| Inflammatory pseudotumor | |
| Fibrosing mediastinitis | |
| Sclerosing mesenteritis | |
| Retroperitoneal fibrosis (Ormond’s disease) | |
| Periaortitis /periarteritis | |
| Inflammatory aortic aneurysm | |
| Cutaneous pseudolymphoma | |
| Idiopathic hypertrophic pachymeningitis | |
| Idiopathic tubulointerstitial nephritis | |
| Idiopathic hypocomplementemic tubulointerstitial nephritis with extensive tubulointerstitial deposits | |
| Idiopathic cervical fibrosis | |
| Proposed Names for Commonly-Used Eponyms and Other Terms Frequently Employed in the Description of IgG4-Related Disease | |
| Mikulicz’s disease | IgG4-related dacryoadenitis and sialadenitis |
| Küttner’s tumor | IgG4-related submandibular gland disease |
| Multifocal fibrosclerosis | IgG4-related disease |
| Ormond’s disease | IgG4-related retroperitoneal fibrosis |
| Riedel’s thyroiditis | IgG4-related thyroid disease |