Table 1.

Summary table for sellar/suprasellar chordoma.

Etiology	Acquired; arise from notochord remnant
Incidence	Few cases reported
Gender ratio	Male: Female = 2:1
Age predilection	4th–5th decades of life
Risk factors	Unknown
Treatment	Mainly en-bloc surgical resection with or without radiotherapy
Prognosis	Favorable if extradural in location and fully removed surgically. Overall median survival time following treatment is 6 years.
Findings on imaging	Usually, an intracranial chordoma presents as a midline heterogenous soft tissue mass with internal calcifications due to adjacent bone destruction. Most of the time, it involves the clivus. It is hyperdense to brain parenchyma on CT. Intermediate-low T1 signal and high T2 signal are expected on MRI. Blooming artefact on T2* sequence on gradient-echo MRI may be seen, representing haemorrhage or calcifications from the eroded bony fragments. Variable enhancement is seen following intravenous contrast administration. FDG avid on PET.