. 2018 May 25;16(2):eRC4011. doi: 10.1590/S1679-45082018RC4011

Table 2. Characteristics of 16 cases of Kennedy’s disease described in Brazil.

Characteristics	Results
Mean age of onset of symptoms	35.5 years (14-49)
Mean of CAG repetitions^*	46.72 repetitions (41-53)
Initial symptoms described^†,^‡	Muscle weakness: 3 individuals Gynecomastia: 1 individual Cramps: 1 individual Dysphagia e dysarthria: 1 individual Dysphonia: 1 individual
Gynecomastia	14 of 16 patients
Affected family members^§	Seelfed et al.:⁽ ⁶ ⁾ 10 men with symptoms of SBMA Kaimen-Maciel et al.:⁽ ⁴ ⁾ 7 men with symptoms of SBMA (one was dead)

Only studies by Dias et al.⁽ ² ⁾ and Kouyoumdjan et al.,⁽ ⁷ ⁾ were considered because they reported number of CAG repetitions. The article by Seefeld et al.,⁽ ⁶ ⁾ did not include number of repetitions. Kaimen-Maciel et al.,⁽ ⁴ ⁾ used number of base pairs;

^†

the study by Dias et al.,⁽ ² ⁾ was not included because it does not provide details on initial symptom of patients;

^‡

Kaimen-Maciel et al.,⁽ ⁴ ⁾ described one of the initial symptoms of one patient with “global disability”. This term was not considered because of its imprecise description;

^§

only the study by Seelfed et al.,⁽ ⁶ ⁾ and Kaimen-Maciel et al.,⁽ ⁴ ⁾ reported affected family members.