| hnRNP R |
SMA |
Reduced in motor neuron axons upon SMN depletion |
(Rossoll et al., 2003) |
| HuD/ELAVL4 |
SMA |
Reduced in motor neuron axons upon SMN depletion |
(Fallini et al., 2011) |
| IMP1/ZBP1 |
SMA |
Reduced in motor neuron axons upon SMN depletion |
(Fallini et al., 2014) |
| TDP-43 |
ALS-FUS |
Sequestered in FUS aggregates |
(Kamelgarn et al., 2016) |
| ALS-TDP |
Altered TDP-43 granule size, dynamics and mobility |
(Gopal et al., 2017; Liu-Yesucevitz et al., 2014) |
| FUS |
ALS-FUS |
Altered FUS granule dynamics |
(Murakami et al., 2015; Patel et al., 2015) |
| Staufen1 |
ALS-TDP, ALS-SOD1 |
Reduced synaptic levels |
(Gershoni-Emek et al., 2016) |
| SMN |
ALS-FUS |
Sequestered in FUS aggregates |
(Murakami et al., 2015) |
| ALS-FUS |
Sequestered in FUS aggregates |
(Groen et al., 2013; Murakami et al., 2015) |
| APC |
ALS-FUS |
Sequestered in FUS aggregates |
(Yasuda et al., 2013) |
| FMRP |
ALS-FUS |
Sequestered in FUS aggregates |
(Yasuda et al., 2013) |
| ALS-C9orf72 |
Sequestered in G4C2-containing granules, increased synaptic levels |
(Burguete et al., 2015) |
| ELAVL2 |
ALS-TDP, ALS-SOD1 |
Increased translation |
(Rotem et al., 2017) |
