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. Author manuscript; available in PMC: 2019 Aug 15.
Published in final edited form as: Brain Res. 2018 Apr 30;1693(Pt A):37–42. doi: 10.1016/j.brainres.2018.04.034

Figure 2. FMRP and TDP-43 cause different clinical syndromes during lifespan.

Figure 2

Diseases associated with FMRP: fragile X syndrome (FXS), Fragile X-associated primary ovarian insufficiency (FXPOI), Fragile X-associated tremor/ataxia syndrome (FXTAS). Diseases associated with TDP-43 proteinopathy: amyotrophic lateral sclerosis (ALS) and frontotemporal dementia (FTD). Known mRNA targets known to date, as shown.