The main manifestations of autoimmune polyendocrine syndrome type 1 (APS-1, red box), autoimmune polyendocrine syndrome type 2 (APS-2, blue box) and X-linked immunodysregulation polyendocrinopathy enteropathy (IPEX, green box). Primary adrenal insufficiency and type 1 diabetes are shared between APS-1 and −2, respectively (red-blue box); Type 1 diabetes is shared between Aps-2 and IPEX (blue-green box).