Demographics
|
|
|
|
Sex |
15 F, 3 M |
4 F, 1 M |
p = 1.00 |
Age |
62.1 (7.1) |
51.8 (9.2) |
p = 0.01 |
Race |
12 C, 3 AA, 2 other, and 1 unknown |
2 C, 2 AA, and 1 unknown |
|
Limited versus diffuse |
6 limited, 1 diffuse, and 11 unknown |
5 diffuse |
|
|
Scleroderma disease characteristics
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|
|
|
Raynaud phenomenon |
6 |
2 |
|
Digital ulcers |
1 |
0 |
|
Interstitial lung disease |
5 |
2 |
|
Esophageal involvement |
2 |
0 |
|
|
Symptoms
|
|
|
|
Shortness of breath |
12 |
3 |
|
Chest pain |
2 |
0 |
|
Fever |
2 |
0 |
|
|
Workup
|
|
|
|
Reported hypoxia |
7 |
0 |
|
Pericardial effusion size |
1 small, 12 mod-large, 5 large |
1 mod, 4 large |
|
Right heart failure |
11 |
0 |
|
Tamponade physiology |
2 |
2 |
|
Pulmonary artery hypertension |
14 (2 unknown) |
3 |
p = 0.22 |
PASP by echo (mmHg) |
79.8 ± 45 |
39.7 ± 11 |
p = 0.06 |
WBC (109/L) |
10 ± 5.2 |
8.7 ± 4.8 |
p = 0.56 |
Hgb (g/dL) |
11.6 ± 2.1 |
10.3 ± 2.8 |
p = 0.26 |
Plt (109/L) |
292 ± 126 |
275 ± 150 |
p = 0.79 |
Cr (mg/dL) |
1.2 ± 0.51 |
2.6 ± 2.5 |
p = 0.03 |
BUN (mg/dL) |
22.6 ± 7.7 |
27.5 ± 31 |
p = 0.53 |
AST (U/L) |
17.4 ± 6.5 |
15.5 ± 2 (2 patients) |
|
ALT (U/L) |
25.2 ± 9.1 |
37.5 ± 12 (2 patients) |
|
proBNP (pg/ml) |
4671.6 ± 4011 |
338.5 ± 269 |
p = 0.15 |
ANA |
10 pos, 2 neg |
4 pos, 1 neg |
|
ANA pattern |
2 nucleolar, 4 centromeres, 2 speckled, 1 diffuse, and 1 unknown |
2 nucleolar, 1 speckled, and 1 diffuse |
|
Scl-70 Ab |
12 neg |
4 neg |
|
ESR (mm/hr) |
51.6 ± 31 |
None reported |
|
CRP (mg/dL) |
47 ± 46 |
1.9 (1 patient) |
|
|
Outcomes
|
|
|
|
Readmission in 90 days |
3 readmissions in 2 patients |
1 |
|
Death (as of 2/2017) |
7 (2 during the admission) |
1 |
|