Table 2.
Etiologies of PH in groups 1, 3, and 5.
| PH group | Etiology | n (%) |
|---|---|---|
| Group 1 | IPAH | 67 (40.9) |
| CTD | 43 (26.2) | |
| PoPH | 22 (13.4) | |
| Anorexigen | 14 (8.6) | |
| CHD | 10 (6.1) | |
| HIV | 4 (2.4) | |
| Heritable | 4 (2.4) | |
| Group 3 | COPD | 40 (36.7) |
| CPFE | 37 (33.9) | |
| IPF | 14 (12.8) | |
| Non-IPF ILD | 12 (11) | |
| Other | 6 (5.6) | |
| Group 5 | Sarcoidosis | 10 (40) |
| Hematological disorders | 5 (20) | |
| LAM | 4 (16) | |
| LCH | 3 (12) | |
| Chronic renal failure | 2 (8) | |
| Splenectomy | 1 (4) |
IPAH, idiopathic pulmonary arterial hypertension; CTD, connective tissue disease; PoPH, portopulmonary hypertension; CHD, congenital heart disease; HIV, human immunodeficiency virus; COPD, chronic obstructive pulmonary disease; CPFE, combined pulmonary fibrosis and emphysema; IPF, idiopathic pulmonary fibrosis; ILD, interstitial lung disease; LAM, lymphangioleiomyomatosis; LCH, Langerhans cell histiocytosis.