Table 1.
Types of Interstitial Lung Disease in 126 Adults Admitted to the ICU With Acute Respiratory Failure
| Type of Interstitial Lung Disease | Participants [No. (%)] |
|---|---|
| Idiopathic pulmonary fibrosis | 15 (11.9) |
| Connective tissue disease | 23 (18.3) |
| Rheumatoid arthritis | 7 (5.6) |
| Systemic sclerosis | 9 (7.1) |
| Systemic lupus erythematosus | 1 (0.8) |
| Primary Sjögren syndrome | 1 (0.8) |
| Myositis | 4 (3.2) |
| Mixed connective tissue disease | 1 (0.8) |
| Other interstitial lung disease | 36 (28.6) |
| Idiopathic nonspecific idiopathic pneumonia | 11 (8.7) |
| Hypersensitivity pneumonitis | 13 (10.3) |
| Vasculitis | 1 (0.8) |
| Chronic eosinophilic pneumonia | 1 (0.8) |
| Chemotherapy/radiation therapy | 2 (1.6) |
| Combined pulmonary fibrosis and emphysema | 5 (4.0) |
| Idiopathic pleuroparenchymal fibroelastosis | 1 (0.8) |
| Familial pulmonary fibrosis | 1 (0.8) |
| Inflammatory bowel disease related | 1 (0.8) |
| Unclassifiable idiopathic interstitial pneumoniaa | 52 (41.3) |
a
Based on American Thoracic Society/European Respiratory Society definition of idiopathic interstitial pneumonia with either inadequate or discordant clinical, radiologic, and pathologic data to support a specific interstitial lung disease subtype diagnosis.