Table I.
Characteristics and demographics of EDS patients (n = 40) undergoing elective vascular procedures
| Variable | Value |
|---|---|
| Age – median (IQR) | |
| Age at EDS diagnosis | 25 (16–39) |
| Age at time of first vascular procedure* | 34 (22–40) |
| Gender – No. (%) | |
| Male | 7 (17) |
| Female | 33 (82) |
| Race – No. (%) | |
| Caucasian | 38 (95) |
| African American | 2 (5) |
| EDS subtype†– No. (%) | |
| Classical | 15 (37) |
| Hypermobile | 16 (40) |
| Vascular | 9 (23) |
| Other EDS subtypes | 0 (0) |
| Family history – No. (%) | |
| History of EDS | 12 (31) |
| History of sudden death | 6 (16) |
| History of early CV disease | 12 (31) |
CV, Cardiovascular; EDS, Ehlers-Danlos syndrome; IQR, interquartile range; No., number.
*
Median age at which patients underwent their first endovascular or open vascular procedure.
†
EDS classification defined using the revised nosology of Villefranche.