Table 1.
n | 10 |
Age (years) | 66 (8.2) |
Female (n (%)) | 7 (70) |
BMI (kg/m2) | 29.6 (6.1) |
Lung disease (n (%)) | |
No | 5 (50) |
COPD | 4 (40) |
ILD | 1 (10) |
Scleroderma (n (%)) | 3 (30) |
6-minute walk distance (m) | 306 ± 148.2 |
Functional class (n (%)) | |
1 | 2 (25) |
2 | 4 (50) |
3 | 2 (25) |
TRV (m/s) | 2.7 (+/− 0.5) |
FEV1 (%) | 84 (29.9) |
FVC (%) | 91 (15.0) |
DLco (%) | 49 (20.9) |
Use of medication for ePH | |
Sildenafil | 1 |
Tadalafil* | 7 |
Ambrisentan / Tadalafil | 1 |
Riociguat | 1 |
Tadalafil (40 mg = 6; 20 mg = 1).