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. Author manuscript; available in PMC: 2018 Jul 25.
Published in final edited form as: J Alzheimers Dis. 2018;64(Suppl 1):S481–S489. doi: 10.3233/JAD-179931

Table 1.

Most prevalent tauopathies and associated tau isoforms

Disease Predominant isoform
Primary tauopathies
 PSP 4R
 Argyrophilic grain disease 4R
 Corticobasal degeneration 4R
 Pick’s disease 3R
 FTDP-17 4R/3R
 PEP 4R/3R
 PDC Guam 4R/3R
 Guadeloupean parkinsonism 4R
Secondary tauopathies
 Alzheimer’s disease 4R/3R
 Down’s syndrome 4R/3R