Table 1.
Author | Primary/recurrence (%/%) | Tumor location (%) | Surgery | Surgery + RT | RT | Observation | Radiation dose (range) Gy | Median FU (months) | |
---|---|---|---|---|---|---|---|---|---|
Bonvalot S [7] | 100 (primary) | abd/chest wall (42), LE (23), UE (7), HN (14), trunk (14) | 67 | 13 | – | – | 50 (4–60) | S + RT | 76 |
Stoeckle E [8] | 65/35 | – | 92 | 7 | – | – | 50 (20–60) | S + RT | 123 |
El-Haddad [9] | 48/52 | E (52), trunk (39), HN (9) | 6 | 41 | 4 | 3 | 50.4 (45–60) | S + RT | 88 |
Husain Z [10] | – | LE (20), UE (40), buttock (10), Trunk (20), HN (10) | – | 10 | – | – | 50.7 (44–62) | S + RT | 48 |
Huang K [11] | 75/25 | abd wall (50), LE (18), trunk (11), HN (18), UE (3) | 106 | 25 | – | – | (45–55) | S + RT | 102 |
Ballo MT [12] | 45/55 | abd wall (10), HN (10), trunk (44), buttock (5), UE (18), LE (13) | 122 | 46 | 21 | – | 60 55 |
S + RT RT |
113 |
Gronchi A [13] | 63/27 | abd wall (22), trunk (50), LE (12), UE (8), HN (8) | 172 | 40 | – | – | 57 (45–65) | S + RT | 135 |
Duggal A [14] | 71/29 | UE (34), LE (20), trunk (31), abd wall (3), buttock (12) | 27 | 8 | – | – | 50 (10–64) | S + RT | 68* |
Gluck I [15] | 76/24 | trunk (57), E (13), HN (20), abd/pelvis (10) | 54 | 28 | 13 | – | 56 (50–68) 50 (50–59) |
S + RT RT |
|
JelinekJA [16] | – | abd (17), E (83) | 19 | 35 | – | – | 54 | S + RTa | 38 |
Park HC [17] | – | E (36), HN (16), trunk (32), buttocks (16) | – | 21 | 3 | – | 48 (40–59) | S + RT, RT | 39* |
Lev D [18] | 74/26 | UE (14), LE (16), abd wall (16), trunk (27), intra abd (14), retroperitoneal (6), HN (7) | 94 | 35 | 9 | – | (50–56) | S + RT, RT | 69 |
Phillips SR [19] | 73/27 | abd wall (21), HN (4), trunk (42), UE (9), LE (17) buttock (7) | 73 | – | 2 | 18 | (30–72) | S + RT, RT | 63 |
Mankin HJ [20] | – | UE (7), LE (48), trunk (34), abd wall/pelvis (11) | 185 | 39 | – | – | – | 31 | |
Dalen BP [21] | – | abd wall (24), UE (22), LE (22), trunk (31), HN (1) | 29 | – | 1 | – | – | – | |
Zlotecki RA [22] | 42/58 | UE (42), LE (35), trunk (7), abd (11), HN (5) | – | 65c | – | 54 (50–56) | S + RT, RT | 72 | |
Barbier O [23] | 42/58 | UE (31), LE (58), buttock (11) | – | – | – | 26 | – | 16* | |
Baumert BG [24] | 60/40 | 42 | 68 | – | 59 (3–74) | S + RT | 72 | ||
Fiore M[6] | 65/35 | E (33), trunk (17), HN (4), abd wall (40), intra abd (7) | – | – | – | 83 | – | 33 | |
Merchant NB [25] | 100 (primary) | E (49), trunk (23), abd wall (20), HN(8) | 74 | 31 | – | – | (45–65) | S + RTb | 49 |
Nakayama T [26] | 82/18 | abd wall (18), UE (9), HN (18), LE (46), trunk (9) | 2 | – | 9 | – | – | 56 | |
Pajaras B [27] | 90/10 | abd wall (45), intra abd (15), UE (15), HN (10), LE (10), trunk (5) | 17 | 2 | – | – | 50 (50) | S + RT | 35 |
Pignatti G [28] | 42/58 | UE (30), LE (60), trunk (8), other (2) | 63 | 17 | 0 | 1 | (35–66) | S + RT | 134* |
Schulz-Ertner D [29] | 43/57 | HN (8), UE (25), LE (29), abd wall (10), intra abd (10), trunk (18) | – | 26 | 2 | – | 48 (36–60) | RTb | 46 |
Sharma V [30] | 88/12 | E (45), HN (14), Trunk (14), abd (27) | 15 | 15 | 4 | 8 | 60 (9–70) 50 (40–50) |
S + RT RT |
– |
Shido Y [31] | – | trunk (30), UE (13), LE + buttock (57) | 30 | – | – | – | – | 89 | |
Sorensen A [32] | – | abd(30), extra abd (70) | 44 | 28 | – | – | – | 96 | |
Guney Y [33] | – | UE (29), LE (29), HN (14), buttock (14), trunk (14) | – | 4 | 3 | – | 51 (50–62) 50 (40–50) |
S + RT RT |
16 |
Rudiger HA [34] | 59/41 | UE (31), LE (43), trunk (26) | – | 17 | 17 | – | 50 (24–60) | S + RT | 51* |
Chew C [35] | 36/64 | UE (43), LE (40), HN (17) | – | 40 | 1 | 1 | – | 150 | |
Kriz [36] | 48/52 | E (54) trunk (38) abd wall (8) | – | 37 | 15 | – | 50–60 55–65 |
S + RT RT |
44 |
Zeng [1] | 67/33 | abd wall (27) intra abd (11) trunk (18) E (14) HN (25) buttock (4) | 184 | 39 | – | – | 38–66 | S + RT | 54 |
Prodinger [37] | UE (49) LE (51) | 10 | 17 | – | – | 50–60 | S + RT | 65 | |
Shin [38] | 74/26 | trunk/HN (41) E (59) | 95 | 24 | – | – | 38–70 | S + RT | 82* |
Sri ram [39] | UE (10) HN (23) trunk (18) buttock (14) LE (35) | 48 | 19 | 5 | – | 48 | |||
Keus [40] | 61/39 | UE (32) LE (32) HN (2) trunk (23) abd wall (11) | – | – | 44 | – | 56 | RT | 60 |
Ergen [41] | 20/80 | UE (20) LE (45) trunk (20) intra abd (10) HN (5) | – | 18 | 2 | – | 60 (40–64) | S + RT | 77.5 |
RT = Radiotherapy, S = Surgery, FAP = Familial Adenomatous Polyposis FU: Follow-Up, E = extremity, LE = lower extremity, UE = upper extremity, HN = head and neck, abd = abdominal.
5 patients received intra operative radiotherapy.
Some patients received brachytherapy.
Number of patients receiving S + RT and RT alone.
Mean follow up.