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. 2018 Jun 14;89(6):413–422. doi: 10.1159/000488347

Table 3.

Previous reports of 6 cases with Turner syndrome and hyperinsulinism

Authors [Ref.], year Age at presentation, days X chromosome findings Diazoxide response Treatment
Glassman et al. [7], 1979
 Case 1 90 45,X 80% pancreatectomy
 Case 2 120 45,X leucine-restricted diet
Kizaki et al. [8], 2003 1 45,X/46,X,r(X) not tested corn starch
Alkhayyat et al. [9], 2006 1 45,X/46,X,r(X) + diazoxide
Pietzner et al. [10], 2014 1 45,X/46,X,r(X) + diazoxide
Cappella et al. [11], 2015 330 45,X/46,X,r(X) + diazoxide