Table 3. Individual change in cognitive test scores from baseline to follow-up (day 21-28).
Patient | DCCS Cognitive Flexibility | Flanker Attention/Inhibiton | List Sort Working Memory | Wechsler PSI Processing Speed |
---|---|---|---|---|
1# | N/A | N/A | N/A | N/A |
2 | stable | stable | stable | stable |
3@ | N/A | N/A | N/A | N/A |
4 | stable | stable | stable | stable |
5 | stable | stable | stable | stable |
6 | stable | stable | stable | increase |
7 | increase | stable | stable | stable |
8 | stable | increase | stable | increase |
9 | stable | stable | stable | stable |
10 | stable | stable | stable | decrease |
11* | N/A | increase | increase | increase |
12^ | N/A | N/A | N/A | N/A |
13@ | N/A | N/A | N/A | N/A |
14 | stable | stable | stable | increase |
15$ | N/A | N/A | N/A | N/A |
16 | stable | stable | stable | increase |
17 | stable | stable | stable | stable |
18 | decrease | decrease | decrease | stable |
19^ | N/A | N/A | N/A | N/A |
20 | decrease | stable | increase | increase |
21 | stable | stable | stable | increase |
22^ | N/A | N/A | N/A | N/A |
DCCS = Dimensional Change Card Sort; PSI=Processing Speed Index
Significant increase or decrease in scores was defined as a difference of ≥ .75 SD (11 points) from testing at baseline to Day 28; tests have a normative mean of 100 and SD of 15; higher scores are better
Patient 1 could not complete follow-up cognitive testing due to significant disease progression
Patients 3 and 13 declined to complete follow-up assessments
Patient 11 could not complete one follow-up cognitive flexibility test due to computer problems
Patients 12, 19, and 22 could not complete the cognitive testing due to trisomy 21 due to concerns about comprehending the instructions and ongoing validation of the NIH Toolbox tests in individuals with intellectual disability.18
Patient 15 could not complete the baseline cognitive testing due to significant nausea/illness