Table 2.

Patients characteristics. FEV1 [%] = percent predicted forced expiratory volume in one second. FVC [%] = percent predicted forced vital capacity.

Young Children	Age [months]	Gender	CF Genotype	Weight [%]	Height [%]	CF pathogen*	FEV1 [%]**	FVC [%]**
1	24	F	DELTAF508, DELTAF508	13.7	25.0	Hi	N/A	N/A
2	37	M	DELTAF508, DELTAF508	24.9	66.0	Hi,Sa	N/A	N/A
3	27	M	DELTAF508, R117H	74.9	48.9	Sp	N/A	N/A
4	30	M	DELTAF508, Q493X	15.4	6.5	_	N/A	N/A
5	33	F	DELTAF508, DELTAF508	39.8	41.2	Ox-Sa	N/A	N/A
6	35	M	DELTAF508, DELTAF508	35.5	31.3	Hi	N/A	N/A
7	7	M	D1152H, DELTAF508	26.3	10.5	Sa	N/A	N/A
8	26	F	DELTAF508, R764X	65.1	61.1	Sa	N/A	N/A
9	6	M	DELTAF508, DELTAF508	85.6	82.6	Hi	N/A	N/A
10	6	F	DELTAF508, DELTAF508	94.9	63.9	_	N/A	N/A
Mean ± SD	23 ± 12	60% M		48 ± 30	44 ± 25		N/A	N/A
Adolescents	Age [Years]	Gender	CF Genotype	Weight [%]	Height [%]	CF pathogen*	FEV1 [%]	FVC [%]**
1	8	M	Nt1155insTC / Unknown	6.9	12.1	-	49	79
2	18	M	DELTAF508, DELTAF508	17.5	90.3	Af	75	92
3	16	M	DELTAF508, 2789+5G-A	43.6	41.8	_	93	97
4	17	F	DELTAF508, DELTAF508	42.1	35.4	Sa, Sm	71	89
5	12	F	DELTAF508, DELTAF508	35.5	87.3	A	78	87
6	9	M	DELTAF508, DELTAF508	40.0	44.6	Ox-Sa, Hi	96	104
Mean ± SD	13 ± 4	67% M		30.9 ± 15.1	51.9 ± 30.8		77 ± 17	91 ± 9

^*Hi = Haemophilus influenza, Sa = Staphylococcus aureus, Sp = Streptococcus pyogenes, Ox-Sa = Oxacillin Resistant Staphylococcus aureus, Af = Aspergillus fumigatus, Sm = Stenotrophomonas maltophilia, A = Achromobacter.

^**The infants in this study did not have clinically acquired pulmonary function tests at the time of imaging, which required either anesthesia or sedation and are not generally acquired clinically.