Table 1.

Summary of 15 reports of hemophagocytic syndrome after liver transplantation

First author	No.	Age (years)	Sex	Donor type	Diagnosis	Onset	Causes	Treatment					Prognosis
						(POD)		G-CSF	IVIg	Steroid	Dialysis	Chemotherapy
Chisuwa (8)	1	9 mo	F	Living	Biliary atresia	15	Unknown	–	+	+	PE	Etoposide	Died
	2	11 mo	M	Living	Biliary atresia	134	EBV	+	–	+	–	–	Died
Hardikar (13)	3	26 mo	M	Deceased	Acute liver failure	15	CMV	+	+	–	–	–	Alive
George (9)	4	10	M	Deceased	Acute liver failure	6 years	EBV	–	–	+	+	Etoposide	Alive
Taniai (12)	5	37	F	Living	Unknown	11	Unknown	–	+	+	PE, CHDF	–	Died
Karasu (10)	6	38	M	Living	HBV/HDV	124	Unknown	+	+	–	PE	–	Alive
Akamatsu (14)	7	48	F	Living	LC/HCV	50	HCV	+	–	–	–	–	Died
Dharancy (15)	8	49	F	Deceased	polycystic liver/kidney	12	HHV6	–	–	–	–	–	Died
Akamatsu (14)	9	49	F	Living	PBC	315	CMV	–	+	+	PE	–	Died
Soyama (3)	10	57	M	Living	LC/HCV/HCC	32	CMV/HCC	+	+	+	–	–	Died
Akamatsu (14)	11	59	M	Living	LC/HCV	138	Aspergillus	–	–	–	–	–	Died
Soyama (3)	12	63	M	Living	LC/HCV/HCC	81	Unknown	+	+	+	–	–	Died
Llado (11)	13	63	M	Deceased	Autoimmune hepatitis	NA	Unknown	–	+	+	–	–	Died
Yoshizumi (1)	14	63	M	Living	PBC	13	SFSS	+	+	+	–	–	Alive
Present case	15	63	F	Living	HBV	7	SFSS	+	+	+	CHDF	–	Died

CHDF continuous hemodiafiltration, CMV cytomegalovirus, EBV Epstein-Barr virus, G-CSF granulocyte-colony stimulating factor, HBV hepatitis B virus, HCV hepatitis C virus, HCC hepatocellular carcinoma, HDV hepatitis D virus, HHV6 human herpesvirus 6, IVIg intravenous immunoglobulin, LC liver cirrhosis, mo months, NA not available, PBC primary biliary cholangitis, PE plasma exchange, POD postoperative day, SFSS small-for-size syndrome