Table 1. Clinical data of patients with PAH.
| Patient | Age | Sex | Diagnosis | Gene mutation | PAP (s/d/m) | CI | PVR |
|---|---|---|---|---|---|---|---|
| (years old) | (Gene, amino acid change) | (mmHg) | (L/min/m2) | (dyne·sec·cm–5) | |||
| 1 | 31 | F | IPAH | 73/30/48 | 2.1 | 1199 | |
| 2 | 13 | F | IPAH | 111/49/67 | 1.7 | 2438 | |
| 3 | 28 | F | IPAH | 113/36/66 | 1.8 | 3340 | |
| 4 | 43 | F | IPAH | 107/47/72 | 2.4 | 3056 | |
| 5 | 16 | F | IPAH | 83/51/65 | 2.5 | 784 | |
| 6 | 11 | M | IPAH | 130/51/80 | 1.9 | 2629 | |
| 7 | 8 | F | IPAH | 98/54/74 | 3.1 | 1784 | |
| 8 | 10 | F | IPAH | 60/35/45 | 2.8 | 1040 | |
| 9 | 25 | M | IPAH | 77/35/50 | 2.8 | 532 | |
| 10 | 12 | F | HPAH | SMAD9, p.Lys43Glu | 99/59/72 | 2.3 | 2779 |
| 11 | 20 | M | HPAH | BMPR2, p.Leu139Ser | 70/40/50 | 3.3 | 808 |
| 12 | 11 | F | HPAH | BMPR2, p.Arg491Gln | 106/47/67 | 3.2 | 1148 |
PAH: pulmonary arterial hypertension, PAP: pulmonary artery pressure, s/d/m: systolic/diastolic/mean, CI: cardiac index, PVR: pulmonary vascular resistance, F: female, M: male, IPAH: idiopathic pulmonary arterial hypertension, HPAH: heritable pulmonary arterial hypertension.