Abbreviations: AIADK, autoinflammation with arthritis and dyskeratosis; AIFEC, autoinflammation with infantile enterocolitis; AILJK, autoimmune interstitial lung, joint and kidney disease; DIRA, deficiency of IL-1 receptor antagonist; Dysreg, dysregulation (including lymphoproliferation); FCAS2, familial cold autoinflammatory syndrome 2; HIDS, hyper IgD syndrome; HYDM1, hydatidiform molar pregnancy; MSPC, multiple self-healing palmoplantar carcinoma; ORAS, otulin-related autoinflammatory syndrome; PAAND, pyrin-associated autoinflammation with neutrophilic dermatosis; PAPA pyogenic arthritis, pyoderma gangrenosum and acne; RAAS, proteasome associated autoinflammatory syndrome; PRP, pityriasis rubra pilaris; SPENCD, spondyloenchondrodysplasia; XLPDR, x-linked pigmentary disorder, reticulate, with systemic manifestations. Adapted and updated from [101] with permission granted by Springer Nature, licence number: 4371831027106.