Table 2.
Clinical characteristics of the children diagnosed with an inherited cardiac arrhythmia syndrome
| Children diagnosed with an inherited cardiac arrhythmia syndrome (n=47) | |
| Time since diagnosis, days | |
| Mean (SD) | 1444.31 (1062.27) |
| Minimum/maximum (range) | 42/4678 (4636) |
| Diagnosis, n (%) | |
| Long QT syndrome | 29 (62) |
| Brugada syndrome | 11 (23) |
| Catecholaminergic polymorphic ventricular tachycardia | 5 (11) |
| Short QT syndrome | 1 (2) |
| Unknown | 1 (2) |
| Symptoms, n (%) | |
| No | 27 (57) |
| Yes | 20 (43) |
| Out-of-hospital cardiac arrest, n (%) | |
| No | 44 (94) |
| Yes | 3 (6) |
| Treatment, n (%) | |
| None | 13 (28) |
| Medication | 27 (57) |
| Medication+ICD | 7 (15) |
| History of SCD in immediate family, n (%) | |
| No | 41 (87) |
| Yes | 6 (13) |
ICD, implantable cardioverter-defibrillator; SCD, sudden cardiac death.