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. 2018 Aug 30;2(1):e000271. doi: 10.1136/bmjpo-2018-000271

Table 2.

Clinical characteristics of the children diagnosed with an inherited cardiac arrhythmia syndrome

Children diagnosed with an inherited cardiac arrhythmia syndrome (n=47)
Time since diagnosis, days
 Mean (SD) 1444.31 (1062.27)
 Minimum/maximum (range) 42/4678 (4636)
Diagnosis, n (%)
 Long QT syndrome 29 (62)
 Brugada syndrome 11 (23)
 Catecholaminergic polymorphic ventricular tachycardia 5 (11)
 Short QT syndrome 1 (2)
 Unknown 1 (2)
Symptoms, n (%)
 No 27 (57)
 Yes 20 (43)
Out-of-hospital cardiac arrest, n (%)
 No 44 (94)
 Yes 3 (6)
Treatment, n (%)
 None 13 (28)
 Medication 27 (57)
 Medication+ICD 7 (15)
History of SCD in immediate family, n (%)
 No 41 (87)
 Yes 6 (13)

ICD, implantable cardioverter-defibrillator; SCD, sudden cardiac death.