Table 1.
Patient characteristics at first presentation.
| All patients, n = 58 | |
|---|---|
| Age (years), median (range) | 30.1 (18-58) |
| Sex (female : male), % (n) | 58.6 (34) : 41.4 (24) |
| BMI (kg/m2), median (range) | 19.7 (13.7–29.0) |
| Genotype, % (n) | |
| F508del homozygous | 37.9 (22) |
| F508del heterozygous | 43.1 (25) |
| Other (non F508del) | 2.1 (1) |
| Missing | 17.2 (10) |
| Time since last LT (years), median (range) | 2.3 (0.0–15.4) |
| Pancreatic insufficiency, % (n) | 96.6 (56) |
| CFRD, % (n) | 50.0 (29) |
| NODAT, % (n) | 27.6 (16) |
| Osteopenia/osteoporosis, % (n) | 87.9 (51) |
| Vitamin D deficiency, % (n) | 98.1 (53)* |
Asterisk indicates data available for 54 of 58 patients; normal range: 75–250 nmol/L.
BMI: body mass index; LT: lung transplantation; CFRD: cystic fibrosis related diabetes; NODAT: new onset diabetes after transplantation.