Table 2.

Sociodemographic, clinical, and psychological characteristics of DM1 patients.

	All DM1 (n = 31)	Juvenile DM1 (n = 18)	Adult-onset DM1 (n = 9)	Late-onset DM1 (n = 4)
Age (years)	37.0 (25.0–50.0)	29.5 (24.0–40.0)	39.0 (36.0–52.0)	55.0 (48.0–58.5)
Gender (% Male)	61	55.6	55.6	100
Age at onset (n)	20.0 (16.0–25.0)*	16.0 (12.0–20.0)	31.0 (25.0–33.0)	43.0 (41.0–45.0)*
Disease duration (years)	14.0 (6.0–24.0)	15.0 (6.0–24.0)	14.0 (5.0–18.0)	8.0 (2.0–14.0)
CTG REPEAT RANGE (n)
E1 (51–150)	2 (6.5%)	0	0	2 (50.0%)
E2 (151–500)	16 (51.6%)	10 (55.6%)	5 (55.6%)	1 (25.0%)
E3 (501–800)	6 (19.4%)	5 (27.8%)	1 (11.1%)	0
E4 (>800)	3 (9.7%)	2 (11.1%)	1 (11.1%)	0
not determined	4 (12.9%)	1 (5.6%)	2 (22.2%)	1 (25.0%)
MIRS	3.0 (2.0–4.0)	3.0 (2.0–4.0)	4.0 (3.0–4.0)	2.0 (1.0–3.5)
MRC	125.0 (112.0–127.7)	125.0 (111.0–128.0)	122.7 (115.0–125.0)	126.0 (112.8–130.0)
Epworth Sleepiness Scale	6.0 (4.0–9.0)	7.0 (6.0–12.0)	6.0 (4.0–7.0)	5.5 (3.0–6.0)
Education (years)	13.0 (8.0–13.0)	13.0 (13.0–13.0)	13.0 (8.0–16.0)	8.0 (8.0–8.0)
% employed	71.0	72.2	66.7	75
% in a relationship	45.0	22.2	66.7	100
ITALIAN REGION
North	24 (77.4%)	12 (66.7%)	8 (88.9%)	4 (100%)
Center	3 (9.7%)	3 (16.7%)	0	0
South	4 (12.9%)	3 (16.7%)	1 (11.1%)	0
MMSE
% in the norm range	96.8	94.4	100	100
ENB-2
% in the norm range	80.6	72.2	88.9	100
FAB
% in the norm range	71.0	61.1	77.8	100
% upper limits of the norm	16.1	22.2	11.1	0
% lower limits of the norm	9.7	16.7	0	0
% deficit	3.2	0	11.1	0
SCL-90-R
% T-scores in the normal range
Global severity index	80.6	83.3	77.8	75.0
Positive symptom total	87.1	88.9	77.8	100
Positive symptom distress index	83.9	88.9	77.8	75.0
Somatization	83.9	83.3	77.8	100
Obsessive-compulsive	90.3	94.4	77.8	100
Interpersonal sensitivity	80.6	83.3	77.8	75.0
Depression	80.6	88.9	66.7	75.0
Anxiety	96.8	100	88.9	100
Hostility	77.4	83.3	55.6	100
Phobic anxiety	90.3	94.4	77.8	100
Paranoid ideation	83.9	83.3	77.8	100
Psychoticism	83.9	88.9	77.8	75.0

^*Patients excluded since asymptomatic. Median value (interquartile range).